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什么是IgA肾病

2019-10-28 阅读量:4410次
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相信有些患者在出现血尿以及眼睑水肿的症状时,医生一般都会让做肾脏功能方面的检查,这时就可能会被诊断为IgA肾病,这些人群虽然对肾病有大致的了解,但是却不清楚这具体是哪一种肾脏疾病。那么IgA肾病到底是什么疾病呢?

IgA肾病是一组多病因引起的具有相同免疫病理学特征的慢性肾小球疾病,其特点是在肾小球的系膜区有颗粒性IgA沉积,IgA肾病又称BERGER病,是一种特殊类型的肾小球肾炎。IgA肾病多发于儿童和青年,发病前常有上呼吸道感染,病变特点是肾小球系膜增生,用免疫荧光法检查可见系膜区有IgA沉积。80%在16-35岁发病,男多于女。肾小球肾炎类型的疾病虽然类型较为常见,但治疗需根据个体情况制定方案。

IgA肾病的诊断必须要有肾活检病理,必须要有免疫荧光或免疫组化的结果支持。其诊断特点是:光镜下常见弥漫性系膜增生或局灶节段增生性肾小球肾炎;免疫荧光可见系膜区IgA或以IgA为主的免疫复合物沉积,这是IgA肾病的诊断标志。

潜血是IgA肾病的最常见症状,病人可以是单独出现潜血,也可以伴有蛋白尿,同时还可伴有身体部分(腹、腰、嗓子)疼痛、水肿、高血压。IgA肾病潜血可有急性速发性肉眼潜血和发作性肉眼潜血两种。

通过以上介绍我们对于IgA肾病疾病也有了初步的了解,随着医学界对IgA肾病疾病的认识和治疗经验的积累,患者可能会出现不同系统的症状,为此应重视患者的个体化诊疗,帮助患者更好地配合疾病的处理和治疗。

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